Anaesthetic Management in Pierre Robin Sequence with Severe Upper Airway Obstruction: A Case Report

Abstract

Introduction: A rare congenital birth abnormality known as Pierre Robin sequence (PRS) is characterised by an underdeveloped jaw, tongue displacement backward, and obstruction of the upper airway. Early breathing and feeding difficulties are typical in babies with PRS because of the placement of the tongue, the smaller jaw, and the development of a cleft palate. Case presentation: In this report, we will discuss a case of PRS, who had history of recurrent respiratory tract infections present. Also detailing the anaesthetic management of a 2year old child weighing 9.2 kg diagnosed with Pierre Robin sequence (PRS) with severe upper airway obstruction undergoing complete cleft palate posted for tongue lip adhesion release with palatoplasty. Discussion: The procedures mentioned above call for general anaesthesia as an anaesthetic intervention. For patients undergoing computed tomography (CT) and magnetic resonance imaging (MRI), anesthesiology-assisted sedation may be necessary. Conclusion: This study concluded that a PRS patient with a complete cleft palate poses challenges on airway management.