Paediatric Anaesthetic Management of a Child with Goldenhar Syndrome Associated With Persistent Sub Aortic Vsd Posted For Cleft Palate Repair

Abstract

Goldenhar Syndrome (GS), a rare congenital disorder characterized by craniofacial anomalies, presents unique challenges in surgical and anesthetic management, particularly when accompanied by complex cardiac defects. Here, we present the case of a 5-year-old child with GS undergoing cleft palate repair surgery, complicated by Tetralogy of Fallot (TOF) and a large subaortic ventricular septal defect (VSD). Anesthetic management focused on maintaining hemodynamic stability and optimizing oxygenation, considering both the craniofacial abnormalities and the underlying cardiac pathology. The case underscores the importance of tailored perioperative strategies and interdisciplinary collaboration in achieving favorable outcomes for patients with GS and associated cardiac anomalies.